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Vasculitides
Fudanuniversity
ZhongshanHospital
Yuqiang1
Thetermvasculitisrefers
toaheterogeneousgroupof
disorderscharacterized
pathologicallybyevidenceof
bloodvesselinflammationand
clinicallybyadiversesetof
symptomsandsigns.2
Pathology
threetypes:
1.necrotize
2.granulomas
3.onlyinflammatorycellular
infiltrationinthevesselwall
3
Causeto
1.vesselwall
angusty,
blunting、
fibrosis,
aneurysm
2.tissue
ischemia,
functionalimpaiement
4
CLASSIFICATION
1.histopathologic
(1)necrotize
(2)granulomas
(3)leucocytoclasia
(4)giantcell
5
2.clinicalclassific
?infectivity
?un-infectivity6
3.clinical+histopathologic
primarily
skin
systemic
secondary7
LieCLASSIFICATION
primarily
large-vessel
Takayasuartertis
giantcellartertis
Medium-vessel
polyarteritisnodosa
Churg-Strusssyndrom
Wegener’sgranulomatosis
small-vessel
Microscopicpolyangiitis
Schonlein-Henochsyndrom8
Secondary
infectivity
drug
connectivetissuedisease
associatedwithtumer
9
pathogenesis
1.infectivity
2.immunecomplex
3.antineutrophilcytoplasmicantibody
ANCA-PR3
ANCA-MPO
4.antibodyattackvessel
AECA
GBMantibody
5.cellimmune
6.understand10
clinicalmanifestation
fever
debll
generalmalaise、
anaemia、
myosalgia、11
Prompt:
fever
rash
jointpain
myosalgia
organimpaired
12
theChapelHillConsensusConference
199313
giantcellartertis:
Granulomatousarteritis
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