常见的风湿性疾病相关综合征.ppt

风湿性疾病相关综合征的诊治 龙现明 A summary of syndromes (1) Felty syndrome Reiter’s Syndrome (Reactive Arthritis) PONCET syndrome CREST syndrome Churg-Strauss syndrome Hemophagocytic syndrome Macrophage Activation Syndrome SAPHO syndrome Paraneoplastic rheumatologic syndrome POEMS syndrome Ehlers-Danlos syndrome Weber-Christian syndrome A summary of syndromes (2) Sjogren’s syndrome Antiphospholipid syndrome (APS) Bechet’s syndrome RS3PE syndrome Overlap syndrome Raynaud’s syndrome Undifferentiated polyarthritis syndrome Lupus anticoagulant hypoprothrombinemia syndrome (LAHS) Rowell’s syndrome Drug-induced lupus syndromes Cogan’s syndrome Large granular lymphocyte syndrome Caplan’s syndrome Palindromic syndrome Shrinking lung syndrome Thrombotic thrombocytopenic purpura–hemolytic uremic syndrome (TTP-HUS) Neuropsychiatric lupus (NPSLE) syndrome Lambert-Eaton myasthenic syndrome (LEMS) Sweet’s syndrome Chronic Infantile Neurologic Cutaneous and Articular (CINCA) Syndrome Parry-Romberg syndrome Other syndromes Löfgren’s syndrome Hemolytic uremic syndrome HELLP (hemolysis, elevated liver enzymes, low platelets) syndrome Waterhouse-Friderichsen syndrome (WFS) Carpal tunnel syndrome Milwaukee shoulder syndrome Greater trochanteric pain syndrome Femoroacetabular impingement syndrome Demyelinating syndromes Frank nephrotic syndrome Cold agglutinin syndrome Hyperviscosity syndrome Stiff skin syndrome Werner’s syndrome Shulman’s syndrome or fasciitis-panniculitis syndrome Carcinoid syndrome Eosinophilia-myalgia syndrome Chronic fatigue syndrome Toxic oil syndrome Parry-Romberg syndrome Hypocomplementemic urticarial vasculitis syndrome Hypereosinophilic syndrome Papular-purpuric gloves and socks syndrome (PPGSS) Felty’s syndrome 1924年由A.R Felty首先提出，用于描述慢性关节炎、脾大、粒细胞减少三联征 见于血清阳性侵蚀性强的RA，为RA患者罕见的症状群，在美国RA患者中发生的概率约为1-3% RA患者出现FS提示关节炎及关节外表现严重、预后差 Felty’s syndrome (FS)：定义 Felty’s syndrome (FS)：诊断 关节外表现： 类风湿结节（76%） 体重下降（68%） 干燥综合征（56%） 淋巴结肿大（34%） 下肢溃疡（25%） 胸膜炎（19%） 皮肤色素沉着（17%） 周围